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Bicuspid aortic valve – state-of-the-art

Paulina Lis, Piotr Lyzwa, Radoslaw Walczewski, Olga Mozenska, Dariusz A. Kosior

Abstract


Bicuspid aortic valve (BAV) is the most frequent congenital valve disease. Currently, due to proven correlation between BAV and severe complications, including death, it is thought to be an important clinical issue. The review aims to summarize the current state of knowledge about BAV. Based on available literature, BAV epidemiology, morphology, genetics, diagnostic criteria, screening in relatives and most common complications have been described. BAV can be associated with both valve disease and aortic disease, thereby leading to increased morbidity and mortality. Additionally, significant part of the article reviews the mechanisms of formation, phenotypes and treatment of aortic aneurysm in patients with BAV.

Keywords


valvular heart disease, congenital defects, aorta

Full Text:

References


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